D57.42 Sickle-cell thalassemia beta zero without crisis
Instructional Notes:
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D57.42
Description: Sickle-cell thalassemia beta zero without crisis
Inclusion Term:
- HbS-beta zero without crisis
- Sickle-cell beta zero without crisis
↓
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D57.4
Description: Sickle-cell thalassemia
Inclusion Term:
- Sickle-cell beta thalassemia
- Thalassemia Hb-S disease
↓
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D57
Description: Sickle-cell disorders
Exclude1:
- other hemoglobinopathies (D58.-)
Use Additional Code:
- code for any associated fever (R50.81)
↓
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D55-D59
Description: Hemolytic anemias (D55-D59)
↓
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D50-D89
Description: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Exclude2:
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)